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2016

1 : 1


-I 1
- 1 1 . 6
6
2
.
- II
1
:
:
:
5 4 2 1
2

3
:

A
B
C

10
20
45

ADN

ARN

98
0
0

10
84
1

0
97
0

1 , .
:

ARNm
= 0

= 30 ARNm

ARNm

. 2
)2 .
:

5
/



.
ARNm
ARNm
.
2
. :

:( )+
( )-
+
+
+ + ( )DNP
ATP
+
+ ARNm +
+ ARNm + ATP +
3
- 4 ,
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2016

1 : 1

5 .5


.
.
1 ( )1 .

- .
- ) ( 1 ( , )2 .
- ( )5 .
( ) 10 .
2 ()() ( )2 ( )10 .1
1
6

4 +5

3
2

--

--
2

1. 8
- ()() ( )2 .
- () .
- ( )6 (.)2
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2016

1 : 1

( )2 , ( )7
.
3 ( )Gly
( .) Lys .1=PH

- .
( PHi ) . R(Gly)= H. R(Lys)=(CH2)4-NH2

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2016

1 : 1

5 . 3
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2016

1 : 1



.ADN
1 I - .
- 4 ( )1 :
[ ] .

2 - ()1
- .
- . .
- II ADN
1 -
()2
(
) ARN

(. )3
ARNt
- ) ( 4

. -2 - 2 3 4
.
- , .

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2016

1 : 1




-I
. 1
1 1 ( 5)1
1 .6
- 2 4
.
3 4 . 6
- 4 4 .
5 4 AND

II () 2
ARNm
() .
1
--
--
--

1
2
3

5
6

CCC CUC UGU GGU GAU GAA AAA UGC CAU



Pro Leu Cys Gly Asp Glu Lys Cys His
1
2
3
4
5
6
7
8
9
Pro Leu Ala Gly Asp Glu Lys Cys His
1
2
3
4
5
6
7
8
9

1 ()
.2
3 ( )ARNt- Ala
ARNm ( )2 ()
.2
2 3
ALa
.ARNt
Cys
3

( )3
( ) .
Cys Ala
- .

ACA
ACA
4 :
ARNt
:

.
-
3
.
- .

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2016

1 : 1


.
1 ( )1 ARN
.
- 1.9
- .
- . .

2 ( )2 () (.)1
- . 2
.


-

3 ( )3
( )1 .


( )

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2016

1 : 1

.3
- .
- ( )2


( )
.
1 ARN . ARN
.

- ARN
2
()1
( )
.
( )2,1

1
.
-
( )4
(.)C
.
3


.
:
(.)2

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2016

1 : 1



:
()1
) ( )) .

1 - 1. 8
- ( ) () .
-() .
- 2 ( ( () :
6 (). . - 3 ( )1 ()3
(.)4
-
- .
- 4
(. )2
- .
- 1 .2
-
() .

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2016

1 : 1


, :
I ( ) .
,
( )1 (. )1
( )2 ( )1 .

1
4
ARNm



10
10

1
1

1 ( )1 (: )1
-
- .
2 1 , 5 ( )2 (.)1
3 () , (.)2
4 () , .
5 ( )1 (, )4 .
II :

(
) .
( )2 E1
241 . 245

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10

2016

1 : 1

1 (.)2
2 , E1
ADN .
( )3

.
3 ,

.
3

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11

1 : 1

2016


.
I
() 1 () 1
.
1 . 1
-2 . 1
3 () .
7

9
10

1
11

- II () 1 .
:
: 1


(
:
)
406
ATP + ARNm +
1
1 .
15
ATP + ARNm
2
2
50
ARNm +
3
3
5
ATP +
4
.
: 2
( )1(: )2

( )1( )2 2

( )1( )2
2
( )1( )2
1.5
.
1
( )1 ( )2( .)ARNt
1
0.5

( )1( )2
51
10 15
20
25

. 2

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12

2016

1 : 1

1 ( )1()2
.
2
III ( )3
II
.
1 .
2 .3
3 .
4


, ADN .
- I ( 1,) .

1 1 . 10
2 (-1) (-1) .
- 3 (-1) -
.
4 - (-1) .
-
- II : () 20 (
) . :
1960 ARNm
. ARN
. .
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13

2016

1 : 1

.
ARNm
( -2) ( -2).
- 1
- 2 .
- III II , I :
" ADN ".


ARNm ADN .
1 .
1 : 1
. 1
.
- .
-2 1 2
X
. A
1

.
-2 2 3
X . B

. X
A
. B

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14

2016

1 : 1

. .
-3 ADN
: ADN
C T T A C G G C C T C G

1 2 3 4 5 6 7 8 9 10 11 12
* :
: 8 ( . ) T
: ( ) C 6 . 7
: 7 .
-1 ADN
-2 .
-3 , , ARNm
ADN .
-4 ADN , , , ARNm
, .

( ) Ala

( ) Arg

Asn

Asp

Glu

Cys

GCU,
GCC,
GCA,
GCG

CGU, CGC,
CGA, CGG,
AGA, AGC

AAU,
AGC

GAU,
GAC

GAA,
GAG

UGU,UGC

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Gly
Gln

CAA,
CAG

GGU,
GGC,
GGA,
GGG

15

2016

1 : 1

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16

2016

1 : 1


.
:
- 1 ( )1 .

.
) ( 1
(.)1
- 2

()2

2 . .
3
( ) .

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17

2016

1 : 1

- 3 ) ).


:
- 1 - ) ( 1 .

1 -
.
. ( )2 .

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18

2016

1 : 1

-
-
- 2 ) ( 3 ( )ARNm

1 5 A b (.)3
- ) ( 3 .
- 3 .
. - II , .

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19

2016

1 : 1



(. )01

()01
-1
-2 ( )01 ADN ARNm .
-3 .
-4 UUU . Phe
- 5 ( , , ) ( 2 3 ) 4

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20

2016

1 : 1


) 1 "
- 1 .

- 1

1 .
2 - 1 .
,

, - 2 .

- 2

1
, .
2 .
3 .

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21

1 : 1

2016

1


2

.

3
1
2
3

:
/
/
/
/
/
/
;;
::
::
::

) 2 , " " .

:

- - -
: 1

-1
8

1
GAU

GAG

UGU

AGA

AGA

CGA

CAC

-2 ( ADN )
- 3 -2- .
)
) ( , ) . 2
) ( )7 2

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UCG
3

22

2016

1 : 1


.
.
-1 , , ( 1 )1
( 2 .)1

, ,
. 2.

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23

2016

1 : 1

( 1 )2 . -3 ARN ADN . 3
. ARN
- 1 2 . 3
- (. )3
- ADN .
- 3 4 .

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24

2016

1 : 1


- I ADN
.
( ) 1 () .

1 1 6 (--).
2 ( , )2 ( )2( )5 (.)1

2
3 ( )2 ( )3
.
4 () .
5 .
II ( , )Gly .
1= PH NaOH
PH
PH
()-X-
()
PH ( )y- (.)3
1
2 Phi.
()
3 (--) .
()
. R=H

3
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25

2016

1 : 1

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26

1 : 1

2016


.
.
I ( -1) ARN
.ARNt
( -1) .
1 - () () ( -1) .
ARNt .
2 ( -1)

- . .

- 1

- 1

II )Deficit immunitaire combine severe( Dics-x


(
.).. .
:
T . ()
( )2 ()
Dics-x.

1

T

()

()

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27

1 : 1

2016

1 , ( )2 .Dics-x.
( )3 1
( ) ( ).

() :
862

870

() :

ACU
ACC
ACA
ACG
GGU
GGC
GGA
GGG

UAA
UAG
UGA
GCU
GCC
GCA
GCG

Thr

GLy

ALa

CCU
CCC
CCA
CCG

Pro

CGU
CGC
CGA
CGG

Arg

AUU
AUC
AUA
UCU
UCC
UCA
UCG

Ile

Ser

2 2 3 Dics-x
1 . T


, :
(: )1
() : 6

--
.
() :

1 ,


2 ( )2
122
--
.
(.)2
1
- (.)2
-
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28

2016

1 : 1

( 5. )7
. 2

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29

2016

1 : 1


1 I :
1 2 3 4 5
6
2 :
()




II
:
1

ADN ( )%98 )%10( ARN


()%97
ARN ( )%84
.ARNr
ARNm
.
()%45
()

:
2 : 2
ARN :
= 0 = 30 ARN
ARN.
= 30 ARNm ( )
ARNm .
:
ARN . ARN
.
:
3 :
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30

2016

1
2
3
4
5

1 : 1






DNP
ATP

.

+ ARNm

+ ARNm + ATP+

4 :
( ARNt) + Mg++ PO-4


-1
2 ARN -3 4
( ADN 1)
6 ARNm 5 -9 ATP 8 ARNt -7
10

9/

:
: 1
: ARN (.)ADN
ADN .: 2
: . - ARNm :
ADN . ADN .
- ( ) 10 :
.
.
. :
.
( )

:

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31

2016

1 : 1


()
.
(
.)3
2 1: 8
1 () 2 ARNt ATP 3
6 ( ) ARNm -8 ARNt 7

2Pi 5 AMP -4

- :
() :
: - : ARNt - ( ARNt - ) ATP () :
: - : ( - )ARNm - ( ) ARNt - () ( ) ARNt
:
: 1 : ( ARNt ARNt () ATP
: 2 ( : ) ARNt- ARNt ATP -
.
: 3 : ATP ARNt
: ( ARNt ) ARNt-
- (: )6
ARNt .
ARNt
P A.

- ( ARNt)7 :
ARNt ARNt .

ARN (.)ARNm
3 :
H Gly+
. ( ) . Lys+2

.
+

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32

2016

1 : 1

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33

2016

1 : 1

5
22
= 3+ 3x22 +
3 = 72=3+3+66


- 1 1 :5 .ARNt 1 : 6
1 ( -2 )phe -3 5 ARNt -4 ARNm 6
- 2 4 :
ARNt 20 20= ARNt
3 ARNt : ARNm
- ARNm A : ARNt U

G .C
4 ARNt :
-

ARNt :
.
ARNm

- 5 4 ADN :
ARNt ( ADN ARNt U )T
-1- II ()
:2
GGG GAG ACA CCA CTA CTT TTT ACG GTA 2 :ARNt
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34

2016

1 : 1

3 Cys Ala ARNt 3 ( )- (-: )-


. 3 Cys .Ala - :
.ARNm Cys Ala ARNt Cys Ala.
4 :
ARNm ARNt .
:
. :
( ). - :
- :


1 - :
-4
3
1 2
7
6
5
- :
() : 3,2,1: ( ARNr) 4 ( ARNt)
() : 4,3,2,1 5 ( ARNm). - :
() :
5 () : ARNm . ()
.... . 2 (: )2
:

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35

2016

1 : 1

- , ARNm
, :
.
3 :
:
. - :
ARNm


1 - :
ARNm . - :ARN
ARNm ARNm. 2 .
AUG CUG GUG GAG AGG UGA :
MET-LEU-VAL-GLU-ARG - ( )4 (:)C
( LEU )2 Val () .
( ):
-

( )ADN .

3
:

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36

2016

1 : 1

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37

2016

1 : 1

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38

2016

1 : 1


-1- I - :
( )
- :
:
.
.
2 1: 5
3 ( ARN).
2 ADN 1
5 ADN
4 ADN
( )2 (: )1 ( . ) ARNm
3 () : ARN
ARN : ARN ARNm . ARN ADN . ARN () . ARNm ARN ( ) ADN.
4 () : ARNm
: ( ) ( )
- : - - (.)A.C.U.G
-5 :
ARNm .
II
- 1 ( : )2 ()
- 2 :E1
UUU UCA CAC UCU AAA : ARNm : : -3 :
:
GT 242 GT 243 TG T 242 G 243 TG 243 :
243 UAA 244 . - ( ) .

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39

2016

1 : 1


1 I : 1
-2 3 -4 ADN - 5
1
6 7 ARN -8 -9 -10
ARNm 11
2 : 1

3 () : :
: ARN ADN .
ADN . ARN
ADN .
: ARN ADN ARN
ADN.
: ARNm ADN
ADN .
ATP .
- II : 1
1 :
( : )1 .
( : )2 .
( : )3 .ATP
( : )4 . ARNm
2 :
+ + ATP ARNm
3 :
: ATP .
: ARNm ( ) .
: 2
1 :
( ) 1
( )2 .
2 :
( ) 1 .
( ) 2
ARNt ( ).
1- III :
4 -5
-2 ADN 1 ARN ARNm - 3
2 :
3 :
:
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40

2016

1 : 1

.
4 :

ADN .

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41

2016

1 : 1

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42

2016

1 : 1


1 :
: 1
:ARNm 2 0 2 .
: 4 . 4
: ADN .8
:
:ARNm .
: 4 .
: ADN 8 .
.
: .
- ARNm : . ADN
-2
1 :
Arg
Cys
Try
Val
Cys
Try
Val
ARNm

GUC

UGG

UGU

GUC

UGG

UGU

CGU

ADN

CAG

ACC

ACA

CAG

ACC

ACA

GCA

ADN

GTC

TGG

TGT

GTC

TGG

TGT

CGT

-2
: X

ATT CAA

GCA ACA ACC CAG ACA

UAA GUU

CGU UGU UGG GUC UGU

ARNm

Cys

Val

Try

Cys

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Arg

43

1 : 1

2016

A : B
1 5 5 B
A 6 . 7
: ACC ATT
:
CAG

ACC

ACA

CAG

ACC

ACA

GCA

GTC

TGG

TGT

GTC

TGG

TGT

CGT

CAA

ATT

ACA

CAG

ACC

ACA

GCA

TGT

GTC

TGG

TGT

CGT

: -3
-1 : ADN .
-2 :
.
-3 : ARNm

G ADN

ARNm

T
A

G
C

A
A

ADN :
G A A U G C C G G A G C

ARNm

Arg

Asn

Glu

Cys

-4 ADN , :
: ARNm
:
A C G
G T C T C G
1
G C
ARNm
Asn

2

ARNm

T
A

C A

C
G

Glu

ARNm

Gln

G
Cys

C G
C

C G

Arg

T
A

C
G
Gly

C
G

G
C

C
G
Cys

C
G
Cys

A
Glu

A
U

T
A

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T
A
Glu

T
A
Glu

C
G

44

2016

1 : 1

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45

2016

1 : 1


.ARN

.
:
ARNm .
ARNm .

- 2 - ) ( 2 .
POLYSOMES ARNm
. ARNm . ( ).
:
1
- 2
ARNm 3
-7
ARNt -6
5 ()A
4 ()p
-9
8
:

- 3 .

.

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46

2016

1 : 1


1 - .

:
: . - :
ARNm .
2 :
-3
-2
1
A ARNt .
p ARNt .
ARNm -5 ARNt 4
:
.
ARN- : ( )
: . AUG
- II :

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47

2016

1 : 1

-1 20 :
4 :
-2 ( )01 ADN
: ADN . T
-3
:
: 1 4 (.
=) 4
: 16 = 2 4 (.
)16
: 64
20)64 = 3 4( .
-4 UUU : Phe
ATP ARN
( ) ( ) ARNm

:
( (
:
UUU ARNm ( ) Phe

-5 ( ) ( 2 3 . ) 4

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48

1 : 1

2016


) 1 1 -
2
1
2
1

2
- )2

: ARNm
( ) .
: . ARNm
" ARNm ARNase
.


.
: .
: ARNm
.


1
ACA CUC CUA

GCU UCU UCU

AGC GUG

AND
GAT

GAG

TGT

TCG CAC CGA AGA AGA

3
2 ADN 1
ARNt 5
9

3 ARNm
6
10

7
11

ARNp

ARNt
8

ADN
ARNpm
ARNm
ARNt

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49

2016

1 : 1

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50

2016

1 : 1

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51

2016

1 : 1

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52

2016

1 : 1

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53

2016

1 : 1


-1 I - () () ( -1) :
" " : .
" " : .
- : ARNt
ARNt
:
.

ARNm .
2 ( -1) :
( ARNt )

: ARNt
( .) ARNm
( ).

- :

( " )ARNt .
ARNt .
ARNt ARNm ,
ADN
. ARNm
-1 II : Dics-x
T 1 .
- 2 Dics-x :
ARNm :
CCC CGA AUU.........:
PRO - Arg - ILe
CCC UGA AUU.........:
PRO

: ADN G A 865 ( C
T 865 ).
"" ARNm , (
)IL .

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54

2016

1 : 1

ADN
1

ARNm

ARNm

ARNt
ARNm

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55

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