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OSSIFICANS PROGRESSIVA
Presented by
Lindsey Resignato
2 n d p. Anatomy
Mrs. Torres
DEMOGRAPHIC
Genetic disease affecting 1 in 2 million people
No ethnic, racial, or gender patterns
800 confirmed cases across the globe
285 known cases in the United States
TREATMENT
Systemic steroids are sometimes used for acute flare-ups
Iontophoresis with steroids or acetic acid may improve diminished
range of motion
Effective therapies for fibrodysplasia ossificans progressiva may be
based on blocking activinlike kinase-2 or blocking of activin receptor
IA/activinlike kinase 2 signaling
SURGICAL CARE
May require oral surgical and anesthetic procedures to control oral
pain
The importance of a minimally invasive surgical technique and
appropriate anesthetic management has been stressed
he experience using general anesthesia has been favorable, with
awake nasal fiberoptic intubation evaluated as desirable for airway
management