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OcularMotor

Anomalies


102strabismus
Definitions
Orthophoria
Strabismus(squint) misalignment
Heterophoria(phoria) latentsquint,
maintainedbyeffort
Heterotropia(tropia) manifestsquint,
uncontrolledbybinocularvision
Eso Exo Hyper Hypo Incyclo Excyclo
Visualaxis,anatomicalaxis(Anglekappa)
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AnatomyofExtraocular Muscles
4rectusand
2obliquemuscles
anatomy
SpiralofTillaux
innervation
LR 6thCr.N.
SO 4th
others 3rd
Primaryaction majoreffectinprimaryposition
Subsidiaryactions additionaleffects
Musclepulleys
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Listingplane&axesofFick
(ref.Kanski.ClinicalOphthalmology5thed.P517519)
MuscularActionfromtheprimaryposition:
MusclesPrimarySecondary
MRAdduction
LRAbduction
IRDepressionExtorsion&Adduction
SRElevationIntorsion&Adduction
IOExtorsionElevation&Abduction
SOIntorsionDepression&Abduction
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OcularMovements
Ductions:
monoculareyemovementsaroundtheaxesofFick
Ad,abduction,elevation,depression,intortion,andextortion
Agonist:primarymuscle
Synergist:sameeye,samedirection
Antagonist:sameeye,oppositedirection
Versions:
binocular simutaneous,conjugatemovement
Dextro (right),laevo(left),upgaze,downgaze 2
nd
position
Dextro orlaevo elevation/depression 3rdposition
Dextro orlaevo cycloversion
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OcularMovements
Vergences:
disjunctive(disjugate)binocular movement,
oppositedirection
Convergence(reflexorvoluntary)ordivergence
FourcomponentsofReflexconvergence:
Tonic:MR
Proximal:nearobject
Fusional :binocularsinglevision
Accommodative:synkineticnearreflex
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9(Diagnostic)PositionsofGaze
Primary(1):
straightahead
Secondary(4):
R,L,U,D
Teritary(4):
U&R,D&R,U&L,
D&L
Cardinal(6)
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Cardinalpositionsandyokemuscles
(synergisticmusclesintwoeyes,
primemoversinagivenpositionofgaze)
RSRRIO
LIO LSR
OD RLR RMR OS
R LMR LLR L
RIRRSO
LSO LIR
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SherringtonsLaw
theextraocularmuscles
showreciprocal
innervationof
antagonisticmuscles
(except:Duanesyn)
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Herings Law
equalandsimultaneous
innervationflowsto
synergistic muscles
concernedwiththe
desireddirectionofgaze
(except:Dissociated
VerticalDeviation)
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ClinicalapplicationofHerings Law
Primarydeviation:
thenormaleyefixing
Secondarydeviation:
thepareticeyefixing
For palsy
Acute stage: 2
nd
>1
st
Chronic stage: 2
nd
1
st
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SensoryFusionwithBinocularVision
Firstdegree fusion:
simultaneous
perception
Seconddegree fusion:
flatfusion
Thirddegreefusion:
stereopsis
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FunctionalConsequencesofStrabismus
Amblyopia
Confusion two
dissimilarimagesattwo
foveae
Diplopia twoimagesof
thesameobject
Sensoryadaptationto
strabismus
Suppression
Abnormalretinal
correspondence(ARC)
Motoradaptationto
strabismus
Faceturn,chinupor
down,headtilt
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Examination
History
Familyhistory,ageofonset,typeofonset,typeof
deviation,fixation,predisposingfactors
Visualacuity
Refractiveerror(withmydriactics)
Inspection
Ocularexamination
Slitlamp
fundus
specialexam
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MeasurementofDeviation
Corneallightreflex(reflection)tests
Hirschbergsmethod
modifiedKrimskys method
Brucknertest
Majoramblyoscope method
Covertest
Covertest:tropia
Uncovertest:phoria
Alternatecover(prismandcover)test:tropia
plusphoria
Simultaneousprismcovertest
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Hirschbergtest
Pseudoesotropia epicanthicfolds,short
interpupillarydistance,negativeanglekappa
Pseudoexotropia wideinterpupillarydistance,
positiveanglekappa
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Angle kappa
Positive angle kappa retinopathy of prematurity
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cover /uncover test
Indication:notamblyopic,cooperativetofixationonatarget
Uncover test:
check the covered eye
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Alternate cover test:
measure total deviation
Indication Corneallight
reflex
Cover/Uncover Alternate
Cover
Sensory
Fusion
Orthotropia Straight Noshift Noshift Yes
Phoria Straight Noshift Shift Yes
Tropia Deviation Shift Shift No
Monofixation Smalldeviation Smallshift Largershift Yes
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Krimsky testPrismCovertest
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Prismdiopter()
unitofprismpower
theamountofdeviationproducedbyalightray
transversestheprism
Centimetersofdeflectionmeasured100cmfrom
theprism
Foranglesunder100(45),each2 (1.7pd)are
approximatelyequalto1.
cm=prismdiopter

100cm
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FresnelPrism
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SensoryExamination
Stereopsistests
Randomdotstereograms
Disparateimagewithpolaroidglassed
Suppressiontests
Worth4dottest
Bagolini striatedglasstest
ARCtests
Afterimagetest
Bagolini striatedglasstest
Amblyoscope
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Disparateimagewithpolaroid
glassed:Titmus test
Randomdotstereograms:
TNOtest
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Amblyoscope ()
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Maddoxrodtest
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Worth4dotstest
No change
2 Red or 3 Green:
suppression
2 Red and 3 Green
diplopia (crossing-
XT)
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ChildhoodEsotropia (ET)
Pseudoesotropia widernasalbridge
InfantileET
AccommodativeET
Refractive
nonrefractive
mixed
NonaccommodativeET
Sensorydeprivation
divergenceinsufficiency
stressinduced
sixthnervepalsy
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EssentialInfantileEsotropia
Onset<6m/o
deviation 30pd
usuallycomitant
associatedwithDVDorInferiorOblique
Overaction
associatedwithnystagmus
lowtomoderatehyperopia(<3D)
crossfixationforlargeangleET
bilateralequalvision
Amblyopia(40%)
Tx:surgery(before2y/o)
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AccommodativeET
RefractiveAcc ET
excessivehypermetropia (+4~+7D)
normalAC/Aratio(Distancenear<10PD)
Tx:spectacles(sameatnear&far)
Nonrefractive Acc ET
normalrefraction(<+3D)
highAC/Aratio(Distance:littleornoET)
Tx:nearspectacles
MixedAcc ET
combinedhypermetropia andhighAC/A
ratio
Distance:ET&markedETfornear
Tx:bifocalspectacles
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Childhood Exotropia (XT)
Pseudoexotropia
positiveanglekappa
widerinterpupillarydistance
Intermittent&Constant
BasicXT(Near=Distance)
Divergenceexcess(worseforD.)
Convergenceinsufficiency (worseforN.)
Pseudodivergenceexcess
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CongenitalXT
Presentatbirth(incontrasttoinfantileesotropia)
largeandconstantangle
homonymousfixation
uncommonamblyopia
normalrefraction
associatedwithneurologicalabnormality(in
contrasttoinfantileesotropia)
Tx:surgery
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IntermittentXT
Fluctation betweenphoria andtropia
mostonsetaround2y/o
precipitatedbybrightlight,daydreaming,
fatigue,illness,visualdistraction
withtimepassing,angle&timeofXT
increase
rareamblyopia
Tx:spectacles,
orthoptic treatment,
surgery
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PrinciplesofStrabismusSurgery
Weakeningprocedures
recession
marginalmyotomy
myectomy
posteriorfixationsuture
Strengtheningprocedures
resection
tucking
Advancement
Adjustablesuture
Botulinumtoxinchemodenervation
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DuanesRetractionSyndrome
CongenitalanomalyofinnervationofLR
(absenceof6thneuronswithLR
innervationbybrof3rdnerve)
20%bilateral,femalepredilection,OSmore
Sherringtonslaw()
Severelimitationofabduction,variable
abnormalitiesofadduction,global
retractionandnarrowingofpalpebral
fissureonadduction,up ordownshoot
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DuanesRetractionSyndrome
Type1.themostcommon:
limitedorabsentabduction
normalormildlylimitedadduction
StraightorslightET
Type2.theleastcommon:
limitedadduction
normalormildlylimitedabduction
straightorslightXT
Type3:
limitedab &adduction
straightorslightesotropia
Mayhaveheadturn
Diplopiaandamblyopiaarerare
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DuanesyndromeType1(OS)
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(Amblyopia)

0.5 ()
0.6 ()
0.7 ()
0.8 ()

Amblyopia
Etiology
Refraction:anisometropia,highrefractive
errors(myopia>6D,hyperopia>3D,astigmatism>2D)
vs.

Strabismus:
Occlusion:ptosis,cornealleucoma,cataract
Timing
Therapy
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