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Content
Amino Acid Metabolism
Nucleotide Metabolism and amino acid derived molecules
Others
3. Alkaptonuria (981-2101)
(a) Branched-chain -keto acid dehydrogenase complex
(b) Homogentisic acid dioxygenase
(c) Alanine transaminase
(d) Glutamine amidotransferase
4. phenylketonuria(982-2101)
(a) Phenylalanine (b) Phenylpyruvate (c) Para-hydroxyphenylpyruvate (d) Phenylacetate
5. 1
ammonia (982-2101)
(a) (b)
(c) urea cycle
(d) blood-brain barrier
6. fumarate (982-2101)
(a) Phenylalanine (b) Alanine (c) Cysteine (d) Serine
7. (982-2101)
(a) Leukotriene (b) Testosterone (c) Insulin (d) Prostaglandin
9. ureaNH4+CO2 ammonia
carbamoyl phosphate synthetase I (971-2101)
(a) (b) ATP
(c) HCO3 NH4+(d) carbamoyl phosphate
-
16. transaminationcoenzyme(90-301)
(a) (riboflavin) (b) (thiamin) (c) (vitamin) B6 (d) B12
21. (932-2101)
(a) Ala (b) Asp (c) Glu (d) Ser
23. ? (931-2101)
(a) ammonia (b) urea (c) glutamine (d) uric acid
p.s. Ans = B
24. NH4+(921-5217)
(a) Histidine (b) Arginine (c) Glutamine (d) Asparagine
35. N2 (932-5217)
(A) arginase (B) glutamate synthase
(C) glutamine synthetase (D) nitrogenase
38. ? (901-015)
(a) Glycine (b) Alanine (c) Tyrosine (d) Lysine
39. cysteine(902-015)
(a) threonine (b) lysine (c) methionine (d) tryptophan
40. B1(92-5217)
(a) lipoic acid (b) pyridoxal phosphate (c) coenzyme A (d) thiamine pyrophosphate
41. B12 : (941-2101)
Aacetyl CoA carboxylase Bpyruvate dehydrogenase
Cmethionine synthase Dxanthine oxidase
42. aromatic(942-5217)
(a) lactate (b) shikimate (c) benzoic acid (d) -ketoglutarate
46. NO(972-2101)
(a) Arginine (b) Tryptophan (c) Lysine (d) Methionine
62. RNA ? (1) adenine (2) guanine (3) cytosine (4) thymine (5) uracil (931-2101)
(a) 1,2,3,4 (b) 1,2,3,5 (C) 1,2,4,5 (d) 1,3,4,5
64. ? (901-015)
(a) Dopa (b) Dopamine (c) Norepinephrine (d) Epinephrine
67. glutathione(911-5217)
(a)
(b) free radicals
(c) hemoglobinmethemoglobin
(d) sulfur conjugates
68. serotonin (921-5217)
A His BPhe CTrp DTyr
72. TyrosinePrecursorNeurotransmitter(922-2101)
(a) -GABA BDopamine
(b) Serotonin DAcetylcholine
73. porphyrin(912-5217)
Aleucine Bproline Calanine Dglycine
74. phenylalaninetyrosine(901-015)
(a) (thyroxine) (b) (dopamine) (c) (epinephrine) (d) (corticoid)
77. hypoxanthineaminopterinthymidine
(901-015)
Aacquired immune deficiency syndrome BLesch-Nyhan
Csevere combined immune deficiency syndrome Dgout
86. gout(91-3101)
A pyrimidine B sodium urate C urea
D pH
87. (961-2101)
AAspirin
B Colchicine
C Probenecid
DAllopurinol superoxide dismutase
89. fluorouracil5-FU(912-5217)
Apurine B G2
C D 5-FdUMP
90. 5-fluorourcil5-FU(901-015)
Axanthine oxidase
Bhypoxanthine phosphoribosyl transferaseHPRT
Cdihydrofolate reductase
Dthymidylate synthetase
92. dATP
immunodeficiency(911-5217)
A adenine phosphoribysl transferase Bxanthine oxidase Cadenosine deaminase Dpurine
nucleoside phosphorylase
[H2]: Converts adenosine to
inosine. Enzyme deficiency cause
93. Purine (91-3101) dATP accumulates, which is an
APRPP synthase BHGPRTase CAdenosine deaminase DXanthine oxidase inhibitor of ribonucleotide reductase.
High levels of dATP produce a general
deficiency of other dNTPs in T
lymphocytes.
94. -aminoisobutyrate succinyl [H3]: Soluble end products from
CoA TCA cycle(912-5217) pyrimidine degradation.
Aadenine Bguanine Ccytosine Dthymine [H4]: Degraded to -alanine.
95. biotin(912-5217)
A acetate BCO2 Cmethanol Dphosphate
96. (ribose)(941-2101)
ACoA BNAD CFAD Dthiamine pyrophosphate
Others
99. ATP (952-2101)
(A) creatine phosphate ADP
(B) oxidative phosphorylation
(C) glycolysis
(D) myosin
101. (901-015)
Aglucose Btriacylglycerol C
glycogen D
102. ketoacidosisketone
bodies(911-5217)
A glycolysis
B triacylglyceride
C fatty acids
D gluconeogenesis
103. enzymeglucoselactose
glycolysis(901-015)
Aphosphoglucoisomerase Bphosphofructokinase-1 Cenolase D3-phosphoglycerase kinase
104. ? (901-015)
(a) Avidin (b) Biotin (c) Niacin (d) Thiamin
105. ? (901-015)
(a) Ascobic acid (b) Vitamin A (c) Vitamin E (d) Vitamin K
108. G-(932-5217)
(A) GTP (D) GDP
(C) GTP (D) 7 transmembrane domains