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Olly Congga, Marliyanti Akib, Andi Tenrisanna Devi, Noor Syamsu, Noro Waspodo
Department of Ophthalmology, Faculty Of Medicine, Hasanuddin University
Hasanuddin University Teaching Hospital, Makassar
ABSTRACT
Prior to the
progression of
advanced glaucoma,
the intial
pathophysiology of
her glaucoma
DISCUSSION derived from
common Schwalbe line), with of these conditions trabecular
The lamellae
elevated
complication from the remainder of the under the single and
intraocular eventually
pressures
an incomplete cornea being diagnostic term of separate
she had tofor create
years
development of the normal. Iridocorneal Axenfeld-Rieger the originated
was intertrabecular
from
trabecular adhesions to the syndrome. spaces.
the misalignment
In the
of
meshwork and Schwalbe line range Axenfeld-Riege
anterior segment
Schlemm canal, from threadlike to syndrome,
structures, there
affecting the broad bands of iris Figure 5. Redundant appears
especially to the
be
aqueous outflow tissue.8 The iris itself periumbilical skin variable degrees of
incomplete
facility.3,10-11 markedly atrophic developmentalofarrest
develompent the
Irrespective of with corectopia, In normal in this sequence.
structures that form By
glaucoma, the hole formation, and embryogenesis, the transmission
the conventional
typical corneal stromal iris atrophy. trabecular electron microscopy,
aqueous outflow
abnormality we Dental abnormalities meshwork and the
pathway. trabecular
The
found by and periumbilical Schlemm's canal endothelialorigincells
common of
gonioscopy on both skin were found. In presumably begin as were frequently
Schwalbe's line seen
and
eyes was a posterior view of the above a compact mass of to stroma
iris join fromadjacent
the
embryotoxon (a observations, the cells, which produce connective
neural crest cells
tissue
are
prominent and physician has found the connective tissue cores, toobliterating
thought be due to
anteriorly displaced it useful to place all cores of the the intertrabecular
inadequate
regression of tissues outflow of aqueous Axenfeld-Rieger area and oligodontia
and/or failure in humour was syndrome. Neural are common. Most
differentiation, accumulated in crest cells are often, the maxillary
which results in anterior chamber responsible for deciduous and
distortions of and progressively initiating permanent incisors
normal iridocorneal extended to craniofacial, dental and second
angle anatomy. The posterior chamber, and ocular premolars are
anterior chamber sharing compression development. This missing. The crowns
angle is open and to all of structure. results in of the anterior teeth
gonioscopy shows The weakest part of underdeveloped can be conical or
an anterior insertion posterior chamber, associated neural peg-shaped. Roots
of the peripheral iris the optic nerve, had crest tissues, i.e. the may be shortened,
onto the trabecular the most pressure dental and facial gingival attachments
meshwork. 6,11 back and forth. Thus bones.Inspection of may be reduced and
The globe of the cup and disc the oral cavity may enamel may be
the eye in children is ratio became show microdontia, hypoplastic, all
not as rigid as we glaucomatous and it hypodontia, contributing to poor
have in adult. It is drew the closer oligodontia and a dental health.6,12
naturely elastic. As a retinal layer as we thickened frenulum.
result, it can bear can see in figure 4. In a study by Ozekis
any pressure inside Associated in 1999, 43% of Figure 6.
and decompensates craniofacial patients with Microodontia,
by elongating the abnormalities that Axenfeld-Rieger hypoodontia and
globe structure as it consist of tissues of syndrome had dental oligodontia.
describes the neural crest origin anomalies, while
patophysiology of have long been 25% had facial Other features
advanced glaucoma recognised and can anomalies. that have been
in this case. Initially, assist in making the Underdevelopment reported in
the incomplete diagnosis of of the premaxillary association with the
Axenfeld-Rieger glaucoma associated Axenfeld-Rieger December-2012;
syndrome include with Axenfeld- syndrome. Volume-1; Issue-
redundant Rieger syndrome. 2; 73-74.
periumbilical skin. Others may present 6. Chang TC,
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